What does a double outlet right ventricle mean?
Double outlet right ventricle (DORV) is a type of congenital heart malformation. This means it is present from birth. In this condition, the heart and the main blood vessels leaving the heart do not develop the right way. This can cause symptoms in your child.
What is a double outlet?
In double-outlet right ventricle, the aorta and pulmonary artery connect partially or completely to the right ventricle. A hole also exists between the two ventricles (ventricular septal defect).
What is double outlet right atrium?
Double-outlet right atrium (DORA) is a condition in which the right atrium empties into both ventricles. Described are the anatomic and clinical findings of this rare anomaly and our experience with its surgical treatment.
How rare is DORV?
Double outlet right ventricle (DORV) accounts for about 2-3% of all congenital heart defects, with a birth prevalence rate of 1/ 10,000.
What causes DORV?
Who Gets Double Outlet Right Ventricle (DORV)? In most cases, DORV happens with no known cause. Babies with certain genetic conditions — such as trisomy 13, trisomy 18, or DiGeorge syndrome (22q11. 2 deletion) — are more at risk for DORV.
How do you fix the right ventricle?
Children with double outlet right ventricle (DORV) will need surgery to close the hole in the heart and connect the aorta to the left ventricle and the pulmonary artery to the right ventricle. The most common surgical procedure for DORV with a ventricular septal defect (VSD) is called intraventricular tunnel repair.
How does the right ventricle have a double outlet?
In double-outlet right ventricle, the aorta and pulmonary artery connect partially or completely to the right ventricle. A hole also exists between the two ventricles (ventricular septal defect). In a normal heart, as shown on the left, the pulmonary artery connects to the right ventricle and the aorta connects to the left ventricle.
Is there a hole between the left and right ventricles?
A hole also exists between the two ventricles (ventricular septal defect). In a normal heart, as shown on the left, the pulmonary artery connects to the right ventricle and the aorta connects to the left ventricle.
When do you need surgery for a double ventricle?
Double-outlet right ventricle. Some children will require surgery in the first few days after birth, and others may have surgery at a few months of age. Some people may have other associated congenital heart defects, including other holes in the heart (such as an atrial septal defect), heart valve problems or blood vessel problems.
Can a baby survive with double inlet left ventricle?
Without life-prolonging interventions, the condition is fatal, but with intervention, the newborn may survive. Even if there is no foetal sickness, the diagnosis can be made in utero by foetal echocardiography. Infants born with DILV cannot feed normally (breathlessness) and have difficulty gaining weight.